An Imposter Twice Over: A Case of IgG4-Related Disease
IgG4-RD has the ability to mimic other pathologic conditions, requiring that health care professionals have a high index of suspicion to make a proper diagnosis.
Maj Anna Christensen is a Family Medicine physician, Bhagwan Dass is a Staff Nephrologist, Maj Michael Weisbruch is a Staff Attending in Internal Medicine, and Maj Nathan Kelsey is a Staff Radiologist, all at Eglin Air Force Hospital in Florida. Paulette Hahn is a Clinical Associate Professor at the University of Florida, Department of Medicine, Division of Rheumatology in Gainesville. Correspondence: Maj Christensen (anna.m.christensen2. mil@mail.mil)
Author disclosures The authors report no actual or potential conflicts of interest with regard to this article.
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Conclusion
IgG4-RD is a complicated disease process that requires a high index of suspicion to diagnose. In addition, for patients who are diagnosed with this condition, its ability to mimic other pathologic conditions should be taken into account with manifestation of any new illness. This case emphasizes the ability of this disease to localize in multiple organs over time and the need for lifetimesurveillance in patients with IgG4-RD disease.
